| content | ||||||||||||||||||||||||||||||||||||||||||||||||||||||||||
| Degos disease Classification and external resources |
|
| ICD-9 | 447.8 |
|---|---|
| OMIM | 602248 |
| DiseasesDB | 29425 |
| eMedicine | derm/931 |
| MeSH | D054853 |
Degos disease (also called malignant atrophic papulosis) is an extremely rare vasculopathy that affects the lining of the medium and small veins and arteries, resulting in occlusion (blockage of the vessel). The blood vessels affected include those supplying the skin, gastrointestinal tract, and central nervous system.
The outcome of this disease can be fatal although some appear to have a benign form (Degos acanthoma) which affects only the skin. There are fewer than fifty living patients at present known worldwide.
Contents |
Eponym
It is named for Robert Degos.[1][2]
References
- ^ synd/3466 at Who Named It
- ^ R. Degos, J. Delort, R. Tricot. Dermatite papulosquameuse atrophiante. Bulletin de la Société française de dermatologie et de syphiligraphie et de ses filiales, 1942, 49, 148-150.
Further reading
- Scheinfeld N. Malignant atrophic papulosis. Clinical & Experimental Dermatology. September 2007;5:483-487.
External links
|
|||||||||||||||||||||||||||||||||||||||||
 |
This disease article is a stub. You can help Wikipedia by expanding it. |
